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  2. Keyword: Cardiomyopathy,Restrictive
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Case Report

Transthyretin Amyloidosis (ATTR) – The Role of Multimodality in the Definitive Diagnosis

Tonnison de Oliveira Silva et al. Eduardo Sahade Darze Luiz Eduardo Fonteles Ritt André Luiz Cerqueira Almeida Antônio Ximenes

Introduction

Transthyretin amyloidosis (ATTR) is a rare cause of restrictive cardiomyopathy and/or peripheral polyneuropathy, of a progressive, irreversible and fatal nature, underdiagnosed and with its definitive diagnosis performed late. Early diagnosis, characterization of the type of amyloidosis and subsequent establishment of specific therapy are fundamental for a better prognosis of this disease. We present a case of ATTR where clinical suspicion associated with multimodality diagnosis — nuclear medicine — was able to safely deliver diagnosis, without the need for biopsy.

[…]

  • Amyloidosis/complications
  • Cardiomyopathy,Restrictive
  • Diagnostic Imaging
  • Endomyocardial Fibrosis
  • Heart Failure
  • Hypertension
  • Prealbumin
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Creative Commons Attribution (CC BY) Creative Commons license
18/05/2020 DOI: 10.36660/abc.20180077

How to cite this article

EndNote RIS

Electronic Document Format (Vancouver)

Silva TO, Darze ES, Ritt LEF, Almeida ALC, Ximenes A. Transthyretin Amyloidosis (ATTR) – The Role of Multimodality in the Definitive Diagnosis. Arquivos Brasileiros de Cardiologia 2020;114(4 suppl 1):8-12.

Electronic Document Format (ABNT)

Silva, Tonnison de Oliveira; Darze, Eduardo Sahade; Ritt, Luiz Eduardo Fonteles; Almeida, André Luiz Cerqueira; Ximenes, Antônio. Transthyretin Amyloidosis (ATTR) – The Role of Multimodality in the Definitive Diagnosis. Arquivos Brasileiros de Cardiologia, v. 114, n. 4 suppl 1, p. 8-12, May. 2020.

Electronic Document Format (APA)

Silva, T. O., Darze, E. S., Ritt, L. E. F., Almeida, A. L. C., & Ximenes, A. (2020). Transthyretin Amyloidosis (ATTR) – The Role of Multimodality in the Definitive Diagnosis. Arquivos Brasileiros de Cardiologia, 114(4 suppl 1), 8-12.

Electronic Document Format (ISO)

Silva, Tonnison de Oliveira and Darze, Eduardo Sahade and Ritt, Luiz Eduardo Fonteles and Almeida, André Luiz Cerqueira and Ximenes, Antônio. Transthyretin Amyloidosis (ATTR) – The Role of Multimodality in the Definitive Diagnosis. Arquivos Brasileiros de Cardiologia [online]. 2020, vol. 114, n. 4 suppl 1, [cited 2026-10-14], pp. 8-12. Available from: <https://journals.cardiol.br/en/article/transthyretin-amyloidosis-attr-the-role-of-multimodality-in-the-definitive-diagnosis/>. ISSN 0066-782X

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