Stent Implantation in the Right Ventricular Outflow Tract to Pulmonary Artery in a Child with Pentalogy of Cantrell: Case Report

Introduction

Pentalogy of Cantrell is a syndrome that was first described in 1958. It is characterized by 5 main malformations: defect in the lower sternum, defect in the anterior pericardium, defect in the upper abdomen, deficiency of the anterior diaphragm, and heart defects. The syndrome is rare, with an incidence of 1 in 65,000 live births. It is characterized by midline defects resulting from defective development of the septum transversum. Other congenital heart lesions associated with pentalogy of Cantrell may include atrial septal defect, pulmonary valve stenosis, tetralogy of Fallot, dextrocardia, anomalous pulmonary venous connection, tricuspid atresia, and truncus arteriosus. Children with pentalogy of Cantrell constitute a population with high morbidity and mortality. In this case report, we demonstrate a hemodynamic procedure performed in a patient with this rare congenital anomaly.

[…]