Maria José Morais et al. Fátima Silva Mónica Melo Ana Carriço Francisco Valente
Clinical Case
Fetal cardiac tumors are a rare finding in prenatal ultrasonography with an incidence of 1-2/10000. Rhabdomyomas are the most common tumors in intrauterine life, accounting for 60-86% of primary fetal cardiac tumors.,
According to some case series and mostly case reports, the prevalence of tuberous sclerosis associated with fetal cardiac rhabdomyoma is 50-80%, resulting in a perinatal mortality rate of 0-100%.
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