A Rare Cause of Hypoxemia

Abstract

An unroofed coronary sinus is a very rare cardiac anomaly that is commonly associated with a persistent left superior vena cava. Its diagnosis is often difficult, but clinical signs and echocardiographic findings of an interatrial shunt should raise its suspicion. The authors describe the case of a child with chronic hypoxemia whose diagnostic work-up revealed an unroofed coronary sinus and persistent superior left vena cava.