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  <front>
    <journal-meta>
      <journal-id journal-id-type="publisher-id">abc</journal-id>
      <journal-title-group>
        <journal-title>Arquivos Brasileiros de Cardiologia</journal-title>
        <abbrev-journal-title abbrev-type="publisher">Arq. Bras. Cardiol.</abbrev-journal-title>
      </journal-title-group>
      <issn pub-type="ppub">0066-782X</issn>
      <issn pub-type="epub">1678-4170</issn>
      <publisher>
        <publisher-name>Sociedade Brasileira de Cardiologia - SBC</publisher-name>
        <publisher-loc>S&#227;o Paulo, SP, Brazil</publisher-loc>
      </publisher>
    </journal-meta>
    <article-meta>
      <article-id pub-id-type="publisher-id" specific-use="scielo-v3">cBft3kDZGVnbxNPwm3SjLCF</article-id>
      <article-id pub-id-type="other">00024</article-id>
      <article-id pub-id-type="publisher-id" specific-use="scielo-v2">S0066-782X2010001200024</article-id>
      <article-id pub-id-type="publisher-id" specific-use="scielo-v1">S0066-782X(10)09500224</article-id>
      <article-id pub-id-type="doi">10.1590/S0066-782X2010001200024</article-id>
      <article-categories>
        <subj-group subj-group-type="heading">
          <subject>Relato de Caso</subject>
        </subj-group>
      </article-categories>
      <title-group>
        <article-title>Comunica&#231;&#227;o interatrial e hipertens&#227;o pulmonar em atleta profissional de futebol</article-title>
      </title-group>
      <contrib-group>
        <contrib contrib-type="author">
          <name>
            <surname>Cardoso</surname>
            <given-names>Fernando Bianchini</given-names>
          </name>
          <xref ref-type="aff" rid="aff02"/>
        </contrib>
        <contrib contrib-type="author">
          <name>
            <surname>Cardoso</surname>
            <given-names>Marcos Bianchini</given-names>
          </name>
          <xref ref-type="aff" rid="aff01"/>
        </contrib>
        <contrib contrib-type="author">
          <name>
            <surname>Nishimura</surname>
            <given-names>Roberto Itiro</given-names>
          </name>
          <xref ref-type="aff" rid="aff01"/>
        </contrib>
        <contrib contrib-type="author">
          <name>
            <surname>Ponta</surname>
            <given-names>Georgiane Crespi</given-names>
          </name>
          <xref ref-type="aff" rid="aff03"/>
        </contrib>
        <contrib contrib-type="author">
          <name>
            <surname>Ribeiro</surname>
            <given-names>Gustavo Calado de Aguiar</given-names>
          </name>
          <xref ref-type="aff" rid="aff01"/>
        </contrib>
        <contrib contrib-type="author">
          <name>
            <surname>Costa</surname>
            <given-names>Cledcyson Eloy</given-names>
          </name>
          <xref ref-type="aff" rid="aff01"/>
        </contrib>
      </contrib-group>
      <aff id="aff03">
        <addr-line>
          <named-content content-type="state">S&#227;o Paulo</named-content>
        </addr-line>
        <institution content-type="orgname">Instituto Dante Pazzanese de Cardiologia</institution>
        <country country="BR">Brazil</country>
      </aff>
      <aff id="aff01">
        <addr-line>
          <named-content content-type="state">S&#227;o Paulo</named-content>
        </addr-line>
        <institution content-type="orgname">Pontif&#237;cia Universidade Cat&#243;lica de Campinas</institution>
        <country country="BR">Brazil</country>
      </aff>
      <aff id="aff02">
        <addr-line>
          <named-content content-type="state">S&#227;o Paulo</named-content>
        </addr-line>
        <institution content-type="orgname">Universidade Federal de S&#227;o Paulo</institution>
        <country country="BR">Brazil</country>
      </aff>
      <pub-date date-type="collection" publication-format="electronic">
        <month>08</month>
        <year>2010</year>
      </pub-date>
      <volume>95</volume>
      <issue>2</issue>
      <fpage>38</fpage>
      <lpage>39</lpage>
      <history>
        <date date-type="received">
          <day>22</day>
          <month>08</month>
          <year>2009</year>
        </date>
        <date date-type="accepted">
          <day>14</day>
          <month>12</month>
          <year>2009</year>
        </date>
        <date date-type="rev-recd">
          <day>22</day>
          <month>08</month>
          <year>2009</year>
        </date>
      </history>
      <permissions>
        <license license-type="open-access" xlink:href="http://creativecommons.org/licenses/by-nc/4.0/" xml:lang="en">
          <license-p>This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.</license-p>
        </license>
      </permissions>
      <abstract>
        <p>Relatamos um caso raro de diagn&#243;stico tardio de comunica&#231;&#227;o interatrial (CIA) com hipertens&#227;o pulmonar (HP), atrav&#233;s da ecocardiografia Doppler bidimensional (ECO), em atleta profissional de futebol que ap&#243;s corre&#231;&#227;o cir&#250;rgica retornou ao esporte competitivo de alto rendimento.</p>
      </abstract>
      <kwd-group xml:lang="pt" kwd-group-type="author-generated">
        <kwd>Cardiopatias cong&#234;nitas</kwd>
        <kwd>defeitos do septo interatrial</kwd>
        <kwd>hipertens&#227;o pulmonar</kwd>
        <kwd>ecocardiografia Doppler</kwd>
        <kwd>futebol</kwd>
      </kwd-group>
      <pub-date publication-format="electronic" date-type="pub">
        <day>10</day>
        <month>09</month>
        <year>2010</year>
      </pub-date>
    </article-meta>
  </front>
  <body>
    <p>
      <bold>RELATO DE CASO</bold>
    </p>
    <p>Comunica&#231;&#227;o interatrial e hipertens&#227;o pulmonar em atleta profissional de futebol</p>
    <p>
      <bold>Fernando Bianchini Cardoso<sup>II</sup>; Marcos Bianchini Cardoso<sup>I</sup>; Roberto Itiro Nishimura<sup>I</sup>; Georgiane Crespi Ponta<sup>III</sup>; Gustavo Calado de Aguiar Ribeiro<sup>I</sup>; Cledcyson Eloy Costa<sup>I</sup></bold>
    </p>
    <p><sup>I</sup>Pontif&#237;cia Universidade Cat&#243;lica de Campinas </p>
    <p><sup>II</sup>Campinas, SP; Universidade Federal do Estado de S&#227;o Paulo </p>
    <p><sup>III</sup>Instituto Dante Pazzanesse de Cardiologia, S&#227;o Paulo, SP -Brasil</p>
    <p>
      <xref ref-type="corresp" rid="nt">Correspond&#234;ncia</xref>
    </p>
    <p>
      <bold>RESUMO</bold>
    </p>
    <p>Relatamos um caso raro de diagn&#243;stico tardio de comunica&#231;&#227;o interatrial (CIA) com hipertens&#227;o pulmonar (HP), atrav&#233;s da ecocardiografia Doppler bidimensional (ECO), em atleta profissional de futebol que ap&#243;s corre&#231;&#227;o cir&#250;rgica retornou ao esporte competitivo de alto rendimento.</p>
    <p><bold>Palavras-chave:</bold> Cardiopatias cong&#234;nitas, defeitos do septo interatrial, hipertens&#227;o pulmonar, ecocardiografia Doppler, futebol. </p>
    <p>
      <bold>Introdu&#231;&#227;o</bold>
    </p>
    <p> A comunica&#231;&#227;o interatrial (CIA) &#233; caracterizada pela presen&#231;a de uma comunica&#231;&#227;o entre os &#225;trios por descontinuidade no septo interatrial e &#233; classificada como uma cardiopatia cong&#234;nita acianog&#234;nica com hiperfluxo pulmonar<sup>1</sup>. A maioria dos pacientes &#233; assintom&#225;tica, com indica&#231;&#227;o de tratamento cir&#250;rgico ou por interven&#231;&#227;o percut&#226;nea nos primeiros anos de vida<sup>2-4</sup>. </p>
    <p> As recomenda&#231;&#245;es do &#250;ltimo documento de Bethesda<sup>2</sup> para pr&#225;tica de atividades f&#237;sicas e esportes em indiv&#237;duos portadores de CIA consideram dois grupos distintos, isto &#233;, os tratados cirurgicamente e os n&#227;o tratados. Para aqueles n&#227;o tratados, a presen&#231;a de pequeno defeito septal sem hipertens&#227;o pulmonar (HP) n&#227;o contraindica a participa&#231;&#227;o em nenhum esporte competitivo. J&#225; os indiv&#237;duos que apresentam HP significativa e/ou shunt direita-esquerda, arritmia supraventricular ou ventricular sintom&#225;tica e refluxo mitral significativo dever&#227;o apenas realizar atividades classificadas como classe IA (componentes est&#225;tico e din&#226;mico leves).</p>
    <p> Nos pacientes tratados cirurgicamente ou por interven&#231;&#227;o percut&#226;nea, seis meses ap&#243;s corre&#231;&#227;o e com avalia&#231;&#227;o cl&#237;nica e laboratorial sem evid&#234;ncias de HP, arritmias sintom&#225;ticas ou disfun&#231;&#227;o mioc&#225;rdica, h&#225; libera&#231;&#227;o para a pr&#225;tica de qualquer esporte competitivo.</p>
    <p>
      <bold>Objetivo</bold>
    </p>
    <p> Relatar a import&#226;ncia da ECO em caso de diagn&#243;stico tardio de CIA com HP em atleta profissional de futebol que retornou ao esporte competitivo de alto rendimento ap&#243;s a corre&#231;&#227;o cir&#250;rgica.</p>
    <p>
      <bold>Relato do Caso</bold>
    </p>
    <p> Paciente do sexo masculino, 22 anos, atleta profissional de futebol de campo, assintom&#225;tico, apresentou, durante os exames de pr&#233;-temporada, exame f&#237;sico, eletrocardiograma de repouso e teste ergom&#233;trico m&#225;ximo sem altera&#231;&#245;es. O exame de ECO transtor&#225;cica demonstrou CIA com HP moderada (press&#227;o sist&#243;lica art&#233;ria pulmonar (PSAP) estimada em 56 mmHg), al&#233;m de sobrecarga moderada de c&#226;maras direitas e shunt bidirecional, as altera&#231;&#245;es foram confirmadas pela ECO transesof&#225;gica.</p>
    <p> O paciente foi submetido a tratamento cir&#250;rgico por toracotomia lateral direita, evoluindo sem complica&#231;&#245;es no p&#243;s-operat&#243;rio. Ap&#243;s um m&#234;s da cirurgia, realizou ECO transtor&#225;cica com dilata&#231;&#227;o moderada de ventr&#237;culo direito (36 mm) e PSAP estimada em 37 mmHg. A ECO de esfor&#231;o foi eficaz e revelou PSAP m&#225;xima estimada em 43 mmHg no pico do esfor&#231;o, sem dilata&#231;&#227;o adicional do ventr&#237;culo direito ou d&#233;ficit contr&#225;til. No Teste cardio-pulmonar antingiu 197 bpm com VO<sub>2</sub> m&#225;ximo de 64.31 ml/kg.min. sem altera&#231;&#245;es sugestivas de isquemia e arritmias inexpressivas (cinco extrass&#237;stoles ventriculares isoladas). O Holter de 24 horas evidenciou apenas cinco extrass&#237;stoles supraventriculares isoladas e uma extrass&#237;stole ventricular. Ap&#243;s oito meses, realizou novo ecocardiograma transtor&#225;cico e teste ergom&#233;trico m&#225;ximo sem altera&#231;&#245;es, sendo ent&#227;o liberado para pr&#225;tica esportiva de forma gradativa e com boa evolu&#231;&#227;o ap&#243;s seguimento de 24 meses.</p>
    <p>
      <bold>Discuss&#227;o</bold>
    </p>
    <p> Trata-se de um caso com diagn&#243;stico tardio de cardiopatia cong&#234;nita que somente foi realizado ap&#243;s avalia&#231;&#227;o pr&#233;-participa&#231;&#227;o. </p>
    <p> N&#227;o h&#225; consenso na literatura sobre quais s&#227;o os exames necess&#225;rios para avalia&#231;&#227;o pr&#233;-participa&#231;&#227;o em atletas, sendo que nem sempre a ECO faz parte do arsenal diagn&#243;stico.</p>
    <p> As recomenda&#231;&#245;es da Associa&#231;&#227;o Americana do Cora&#231;&#227;o s&#227;o para realiza&#231;&#227;o apenas de hist&#243;ria m&#233;dica (familiar e pessoal) e exame cl&#237;nico enquanto o consenso da Sociedade Europ&#233;ia de Cardiologia inclui no protocolo de avalia&#231;&#227;o o eletrocardiograma de 12 deriva&#231;&#245;es preferencialmente realizado por especialista em cardiologia ou medicina do esporte<sup>1</sup>. Na It&#225;lia, desde 1971, existe legisla&#231;&#227;o espec&#237;fica federal que obriga a realiza&#231;&#227;o de avalia&#231;&#227;o m&#233;dica pr&#233;via em todos os atletas competitivos, por&#233;m somente a partir de 1994 foi acrescentado &#224; avalia&#231;&#227;o a ECO para atletas de futebol, boxe e ciclismo<sup>1,5,6</sup>. Na Noruega, os atletas profissionais de futebol, e na Alemanha e Fran&#231;a, todos atletas profissionais tamb&#233;m s&#227;o submetidos &#224; ECO durante a avalia&#231;&#227;o pr&#233;-participa&#231;&#227;o<sup>7</sup>.</p>
    <p>
      <bold>Conclus&#227;o</bold>
    </p>
    <p> Este caso demonstrou a import&#226;ncia da realiza&#231;&#227;o desse exame em atletas competitivos, uma vez que ap&#243;s hist&#243;ria, exame cl&#237;nico, eletrocardiograma de repouso e de esfor&#231;o o paciente n&#227;o apresentou nenhuma altera&#231;&#227;o, sendo a doen&#231;a em quest&#227;o somente diagnosticada ap&#243;s a realiza&#231;&#227;o da ECO.</p>
    <p>
      <bold>Potencial Conflito de Interesses</bold>
    </p>
    <p>Declaro n&#227;o haver conflito de interesses pertinentes.</p>
    <p>
      <bold>Fontes de Financiamento</bold>
    </p>
    <p>O presente estudo n&#227;o teve fontes de financiamento externas.</p>
    <p>
      <bold>Vincula&#231;&#227;o Acad&#234;mica</bold>
    </p>
    <p>N&#227;o h&#225; vincula&#231;&#227;o deste estudo a programas de p&#243;s-gradua&#231;&#227;o.</p>
    <p>
      <fn id="nt" fn-type="corresp">
        <p>Correspond&#234;ncia:</p>
        <p>Fernando Bianchini Cardoso </p>
        <p> Rua Teixeira da Silva, 654/71 - Para&#237;so </p>
        <p> 04002-033 - S&#227;o Paulo, SP - Brasil </p>
        <p> E-mail: </p>
        <p>
          <email xlink:href="fernandobcardoso@uol.com.br">fernandobcardoso@uol.com.br</email>
        </p>
      </fn>
    </p>
    <p>Artigo recebido em 22/08/09; revisado recebido em 22/08/09; aceito em 14/12/09.</p>
  </body>
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  </back>
  <sub-article article-type="translation" id="TRen" xml:lang="en">
    <front-stub>
      <article-categories>
        <subj-group subj-group-type="heading">
          <subject>Case Report</subject>
        </subj-group>
      </article-categories>
      <title-group>
        <article-title xml:lang="en">Atrial septal defect and pulmonary hypertension in professional soccer player</article-title>
      </title-group>
      <abstract xml:lang="en">
        <p>This study reports a rare case of late diagnosis of atrial septal defect (ASD) with pulmonary hypertension (PH) through two-dimensional echocardiography (ECHO) in a professional soccer player who resumed high-performance sports activity after surgery.</p>
      </abstract>
      <kwd-group xml:lang="en">
        <kwd>Heart defects, congenital</kwd>
        <kwd>heart septal defects, atrial</kwd>
        <kwd>hypertension, pulmonary</kwd>
        <kwd>echocardiography, Doppler</kwd>
        <kwd>soccer</kwd>
      </kwd-group>
    </front-stub>
    <body>
      <p>
        <bold>CASE REPORT</bold>
      </p>
      <p><undefined id="tx-body2"/>Atrial septal defect and pulmonary hypertension in professional soccer player</p>
      <p>
        <bold>Fernando Bianchini Cardoso<sup>II</sup>; Marcos Bianchini Cardoso<sup>I</sup>; Roberto Itiro Nishimura<sup>I</sup>; Georgiane Crespi Ponta<sup>III</sup>; Gustavo Calado de Aguiar Ribeiro<sup>I</sup>; Cledcyson Eloy Costa<sup>I</sup></bold>
      </p>
      <p><sup>I</sup>Pontif&#237;cia Universidade Cat&#243;lica de Campinas, Campinas, SP</p>
      <p><sup>II</sup>Universidade Federal do Estado de S&#227;o Paulo</p>
      <p><sup>III</sup>Instituto Dante Pazzanesse de Cardiologia, S&#227;o Paulo, SP - Brazil</p>
      <p>Mailing address</p>
      <p>
        <bold>ABSTRACT</bold>
      </p>
      <p>This study reports a rare case of late diagnosis of atrial septal defect (ASD) with pulmonary hypertension (PH) through two-dimensional echocardiography (ECHO) in a professional soccer player who resumed high-performance sports activity after surgery.</p>
      <p><bold>Key Words:</bold> Heart defects, congenital; heart septal defects, atrial; hypertension, pulmonary; echocardiography, Doppler; soccer.</p>
      <p>
        <bold>Introduction</bold>
      </p>
      <p>Atrial septal defect (ASD) is characterized by the presence of a communication between the atria due to discontinuity in the atrial septum and is classified as a congenital heart defect with increased pulmonary flow<sup>1</sup>. Most patients are asymptomatic, with indication of surgical or percutaneous intervention in the first years of life<sup>2-4</sup>. </p>
      <p>The recommendations of the last document by Bethesda<sup>2 </sup>for physical activity and sports in individuals with ASD consider two distinct groups, i.e., those surgically treated and untreate<sup>d</sup>. For those not treated, the presence of a small septal defect without pulmonary hypertension (PH) does not contraindicates participation in any competitive sport. Those individuals who have significant PH and/or right to left shunt, symptomatic ventricular or supraventricular arrhythmia and significant mitral regurgitation should only engage in activities classified as IA Class (light static and dynamic components).</p>
      <p>Patients treated surgically or by percutaneous intervention, six months after repair and clinical and laboratory evaluation with no evidence of PH, symptomatic arrhythmias or myocardial dysfunction, are allowed to practice any competitive sport.</p>
      <p>
        <bold>Purpose</bold>
      </p>
      <p>Report the importance of echocardiogram in late diagnosis of ASD with PH in professional soccer player who returned to high-performance competitive sports after surgery.</p>
      <p>
        <bold>Case Report</bold>
      </p>
      <p>Male patient, 22 years old, professional soccer player, asymptomatic, presented pre-season physical examination, electrocardiogram at rest and maximal exercise testing without abnormalities. Transthoracic echocardiography examination showed ASD with moderate PH (systolic Pulmonary Artery Pressure (sPAP) estimated at 56 mmHg), and moderate overload on right chambers and bidirectional shunting. These findings were confirmed by transesophageal echocardiography.</p>
      <p>The patient underwent surgery for right lateral thoracotomy, evolving without complications in the postoperative period. One month after surgery, the patient performed transthoracic echocardiography with moderate dilation on the right ventricle (36 mm) and aPAP estimated at 37 mmHg. The stress echocardiogram was effective and revealed maximum sPAP estimated at 43 mmHg at peak stress, with no additional dilation of the right ventricle or contractile deficit. In the cardiopulmonary test, the patient reached 197 bpm with maximum VO<sub>2 </sub>of 64.31 ml/kg.min<sub>. </sub>no changes suggesting inexpressive ischemia and arrhythmias (five isolated ventricular extrasystoles). The 24-hour Holter revealed only five isolated supraventricular and ventricular extrasystoles. After eight months, the new transthoracic echocardiography and maximal exercise testing revealed no changes. The patient was then allowed to practice sports in a gradual and progressive way after follow-up of 24 months.</p>
      <p>
        <bold>Discussion</bold>
      </p>
      <p>This is a case with late diagnosis of congenital heart disease that was only done after pre-participation evaluation. </p>
      <p>There is no consensus in literature about which tests are required for pre-participation evaluation in athletes. Echocardiogram is not always part of the diagnostic resources.</p>
      <p>The American Heart Association recommend only examination of medical history (family and personal history) and clinical examination while the consensus of the European Society of Cardiology includes 12-lead electrocardiogram preferably performed by a specialist in cardiology or sports medicine<sup>1</sup>. In Italy, since 1971, there is a specific federal legislation requiring the implementation of prior medical evaluation for all competition athletes, but only in 1994 the echocardiogram was added to the assessment for professional soccer players, boxers and cyclists<sup>1,5,6</sup>. In Norway, professional soccer players, and in Germany and in France, all professional athletes are also assessed by echocardiogram before participating in competitions<sup>7</sup>.</p>
      <p>
        <bold>Conclusion</bold>
      </p>
      <p>This case demonstrated the importance of this examination in competition athletes, because after the determination of history, physical examination, electrocardiogram at rest and stress electrocardiogram the patient showed no changes. The disease involved was only diagnosed after the performance of echocardiogram.</p>
      <p>
        <bold>Potential Conflict of Interest</bold>
      </p>
      <p>No potential conflict of interest relevant to this article was reported.</p>
      <p>
        <bold>Sources of Funding</bold>
      </p>
      <p>There were no external funding sources for this study.</p>
      <p>
        <bold>Study Association</bold>
      </p>
      <p>This study is not associated with any post-graduation program.</p>
      <p>
        <bold>References</bold>
      </p>
    </body>
  </sub-article>
</article>
